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CTG repeat contractions Thérapie génique Glucocorticoids Oligodendrocytes Dystrophie Myotonique Quantitative microdialysis Glucocorticoid-receptor Cell model Male Exercise ACETYLCHOLINESTERASE Mice Lc3 ARN Myotonic dystrophy type 1 DM1 Central nervous system DMSXL mice Muscular dystrophy Brain Antisense oligonucleotide RNA splicing Myotonic Dystrophy type 1 Long read sequencing Cardiac muscle CONGENITAL MYATHENIC SYNDROME Gene therapy AAV Transgenic mouse CMS Exercice Mouse models Mouse model Cell culture model PacBio Glutamate Autophagy Therapy Myotonic dystrophy mouse models DMPK Skeletal muscle Cell penetrating peptide Transcriptomics Intermediate filament Heart failure Fibrosis Humans Knockout Dystrophin MBNL Trinucleotide repeat expansion Acetylcholinesterase knockout mouse Expression CTG repeat instability RNA biology Muscle CRISPR/Cas9 GABA Hypoxia KNOCKOUT MICE Centronuclear myopathy Myelin Aging Heart Astrocytes Diaphragm Dynamin 2 Gene editing Duchenne muscular dystrophy Glial cells Oligodendrocyte Cytoskeleton Astrocyte Myotonic Dystrophy Type 1 BIOLOGIE MOLECULAIRE Trinucleotide Repeat Expansion Dilated cardiomyopathy Antisense oligonucleotides CRISPRi In vivo Myotonic dystrophy Genotype phenotype correlation Animals Acute coronary syndrome Acetylcholinesterase deficiency Myostatin Gene Therapy Desmin RNA interference CTG repeats PCR Transgenic mouse model Myotonic Dystrophy Motoneuron Alternative splicing Maximal force Dystrophie myotonique Brain dysfunction GSK3␤ Neuron