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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
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Chiffres clés
103
Publications avec texte intégral
Open Access
61 %
Mots clés
Thérapie génique
Satellite cells
Pharyngeal muscle
Oculopharyngeal muscular dystrophy
Anti-acetylcholine receptor antibodies
Effector T cells
Duchenne muscular dystrophy
Alzheimer's disease
DMD
Differentiation
Cell therapy
BINDING SPECIFICITY
OPMD
Arbovirus
Xenograft
Anti-fibrotic pharmacotherapies
Cross-bridge kinetics
Mass spectrometry
Geriatric assessment
Metabolism
Regeneration
Muscle stem cells
AAV vectors
Functional genomics
Aged
Accelerometry
Adipose tissue
Nuclear envelope
Alphavirus
Ageing
Aav-U7
Myopathy
Autoimmune diseases
AUTOPHAGY
DNA methylation
ALS
Triplet expansion disease
Muscle dystrophy
FSHD
Dysferlinopathy
Epigenetics
Transcriptomics
GENE
Regulatory T cells
APOPTOSIS
Neuromuscular disease
Neuromuscular junction NMJ
AAV
ARN
Gene replacement
RNA
Myositis
Myoblast
Dystrophin
Annexin A2
Actin
Gene therapy
Aggregate
Biomarker
Dysferlin
Antisens oligonucleotides
Muscle
PABPN1 agregates
Myogenesis
Haploinsufficiency
AChR antibodies
2-D PAGE
Myoblasts
Sarcopenia
Fibrosis
Muscle strength
Amyotrophic Lateral Sclerosis
Inflammation
Antiserum
Intercellular communication
FAPs
DUX4
Satellite cell
Myopathies
Akt
Andermann syndrome
Human
Exon-skipping
Agrégats de PABPN1
Muscle fibrosis
Calcium
Autologous
Bile salt hydrolases
Skeletal muscle
Omics
Lamins
Muscular dystrophy
Myotube
MUTATIONS
Myosin
PABPN1
Dystrophie musculaire oculopharyngée
Atrophy
Regenerative medicine
Pax7